For children with Prader-Willi Syndrome, what is the typical energy need for maintenance?

In children with Prader-Willi Syndrome, the recommended energy needs for maintenance are typically around 10-11 kcal per centimeter of height. This is relevant because Prader-Willi Syndrome is characterized by hypotonia, decreased metabolic rate, and an increased risk of obesity due to their constant hunger and food-seeking behaviors. The guideline for caloric intake is essential to prevent excessive weight gain while ensuring adequate nutrition.

This caloric range reflects a balance where the child's growth and developmental needs can be met without providing excess energy that could lead to obesity. It is important for healthcare providers to tailor dietary plans carefully, keeping in mind the syndrome's metabolic peculiarities. A lower caloric intake than might be expected for height is crucial for managing the condition effectively and promoting healthy growth.